Carnemolla, Alisia; Fossale, Elisa; Agostoni, Elena; Michelazzi, Silvia; Calligaris, Raffaella; De Maso, Luca; Del Sal, Giannino; MacDonald, Marcy E; Persichetti, Francesca
(American Society for Biochemistry and Molecular Biology, 2009-07)
The induction of Rrs1 expression is one of the earliest events detected in a presymptomatic knock-in mouse model of Huntington disease (HD). Rrs1 up-regulation fulfills the HD criteria of dominance, striatal specificity, ...